Pancreatic cystosis: A rare pancreatic manifestation in cystic fibrosis
Cystic fibrosis (CF) is a multisystemic, autosomal recessive disorder that predominantly affects infants, children, and young adults. Manifestations of CF involve the lung and gastrointestinal tract, including the pancreas. Pancreatic cystosis is a rare condition typically seen in CF during the se...
| Main Author: | |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Universiti Kebangsaan Malaysia
2015
|
| Online Access: | http://journalarticle.ukm.my/8788/ http://journalarticle.ukm.my/8788/ http://journalarticle.ukm.my/8788/1/P.307-309.pdf |
| Summary: | Cystic fibrosis (CF) is a multisystemic, autosomal recessive disorder that predominantly affects infants, children, and young
adults. Manifestations of CF involve the lung and gastrointestinal tract, including the pancreas. Pancreatic cystosis is a rare
condition typically seen in CF during the second decade of life. It has characteristic magnetic resonance imaging (MRI) and
ultrasound (US) features. A large cystic mass replacing the pancreas has been found by US and MRI study carried out as a
part of clinical workup for a 17-year-old girl, known to have CF and presented with epigastric pain and a palpable mass.
There was no history of trauma or clinical evidence of pancreatitis. On the basis of MRI findings and the patient age, a
radiological diagnosis of pancreatic cystosis is securely made. Biopsy should be preserved for those who have atypical
presentation. |
|---|