A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy

Paragangliomas are exceptionally rare tumors in children of neural crest origin. Our case report represents an extremely rare location for paraganglioma including its imaging features, perioperative challenges and histopathological characteristics. In the present case, a 10-year-old boy had headache...

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Main Authors:	Dhiraj KB., Mamatha B.
Format:	Article
Language:	English
Published:	Department of Surgery, UKM Medical Centre 2015
Online Access:	http://journalarticle.ukm.my/8658/ http://journalarticle.ukm.my/8658/ http://journalarticle.ukm.my/8658/1/10-%2520Dhiraj%2520%26%2520Mamatha.pdf

id	ukm-8658
recordtype	eprints
spelling	ukm-86582016-12-14T06:47:48Z http://journalarticle.ukm.my/8658/ A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy Dhiraj KB., Mamatha B., Paragangliomas are exceptionally rare tumors in children of neural crest origin. Our case report represents an extremely rare location for paraganglioma including its imaging features, perioperative challenges and histopathological characteristics. In the present case, a 10-year-old boy had headache and blurring of vision for four years but was not diagnosed until he came with malignant hypertension and hypertensive encephalopathy. The symptoms raised urinary catecholamines and CT findings confirmed the diagnosis of a functioning paraganglioma in presacral region. Challenges during surgery are to control the fluctuating blood pressure which may suddenly rise during tumor handling and suddenly fall following its removal. The unusual location of the tumor in pararectal region also made surgical resection difficult. Paragangliomas are rare and should be kept in mind while evaluating a child with hypertension and complete excision is the treatment of choice. Department of Surgery, UKM Medical Centre 2015-06-04 Article PeerReviewed application/pdf en http://journalarticle.ukm.my/8658/1/10-%2520Dhiraj%2520%26%2520Mamatha.pdf Dhiraj KB., and Mamatha B., (2015) A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy. Journal of Surgical Academia, vol.5 (1). pp. 54-57. ISSN 2231-7481 http://jsurgical.com
repository_type	Digital Repository
institution_category	Local University
institution	Universiti Kebangasaan Malaysia
building	UKM Institutional Repository
collection	Online Access
language	English
description	Paragangliomas are exceptionally rare tumors in children of neural crest origin. Our case report represents an extremely rare location for paraganglioma including its imaging features, perioperative challenges and histopathological characteristics. In the present case, a 10-year-old boy had headache and blurring of vision for four years but was not diagnosed until he came with malignant hypertension and hypertensive encephalopathy. The symptoms raised urinary catecholamines and CT findings confirmed the diagnosis of a functioning paraganglioma in presacral region. Challenges during surgery are to control the fluctuating blood pressure which may suddenly rise during tumor handling and suddenly fall following its removal. The unusual location of the tumor in pararectal region also made surgical resection difficult. Paragangliomas are rare and should be kept in mind while evaluating a child with hypertension and complete excision is the treatment of choice.
format	Article
author	Dhiraj KB., Mamatha B.,
spellingShingle	Dhiraj KB., Mamatha B., A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy
author_facet	Dhiraj KB., Mamatha B.,
author_sort	Dhiraj KB.,
title	A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy
title_short	A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy
title_full	A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy
title_fullStr	A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy
title_full_unstemmed	A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy
title_sort	rare case of presacral paraganglioma presenting with hypertensive encephalopathy
publisher	Department of Surgery, UKM Medical Centre
publishDate	2015
url	http://journalarticle.ukm.my/8658/ http://journalarticle.ukm.my/8658/ http://journalarticle.ukm.my/8658/1/10-%2520Dhiraj%2520%26%2520Mamatha.pdf
first_indexed	2023-09-18T19:52:54Z
last_indexed	2023-09-18T19:52:54Z
_version_	1777406337880162304

A Rare Case of Presacral Paraganglioma Presenting with Hypertensive Encephalopathy

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