A rare presentation of plexiform neurofibroma

We report on a rare case of a child with persistent right upper lid eversion with conjunctival prolapse since birth that failed various attempts in repositioning the right superior fornix at other centre. He was found to have a right supero-temporal orbital mass above the prolapsed area. Computerize...

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Main Authors:	Poh, Khay Wei, Syed Osman SIH
Format:	Article
Language:	English
Published:	Pusat Perubatan Universiti Kebangsaan Malaysia 2018
Online Access:	http://journalarticle.ukm.my/12556/ http://journalarticle.ukm.my/12556/ http://journalarticle.ukm.my/12556/1/8._poh__syed.pdf

id	ukm-12556
recordtype	eprints
spelling	ukm-125562019-02-14T21:33:41Z http://journalarticle.ukm.my/12556/ A rare presentation of plexiform neurofibroma Poh, Khay Wei Syed Osman SIH, We report on a rare case of a child with persistent right upper lid eversion with conjunctival prolapse since birth that failed various attempts in repositioning the right superior fornix at other centre. He was found to have a right supero-temporal orbital mass above the prolapsed area. Computerized tomography (CT) scan of orbit confirmed a right lacrimal gland tumour with thinning of the right lesser wing of sphenoid. An excision biopsy of the tumour via anterior orbitotomy and eyelid reconstruction were performed. Histopathology report reviewed plexiform neurofibroma of the lacrimal gland. Further physical examination confirmed presence of multiple café-au-lait spots. He was diagnosed as Neurofibromatosis Type 1. Pusat Perubatan Universiti Kebangsaan Malaysia 2018 Article PeerReviewed application/pdf en http://journalarticle.ukm.my/12556/1/8._poh__syed.pdf Poh, Khay Wei and Syed Osman SIH, (2018) A rare presentation of plexiform neurofibroma. Journal of Surgical Academia, 8 (1). pp. 39-42. ISSN 2231-7481 http://jsurgacad.com/toc/8/1
repository_type	Digital Repository
institution_category	Local University
institution	Universiti Kebangasaan Malaysia
building	UKM Institutional Repository
collection	Online Access
language	English
description	We report on a rare case of a child with persistent right upper lid eversion with conjunctival prolapse since birth that failed various attempts in repositioning the right superior fornix at other centre. He was found to have a right supero-temporal orbital mass above the prolapsed area. Computerized tomography (CT) scan of orbit confirmed a right lacrimal gland tumour with thinning of the right lesser wing of sphenoid. An excision biopsy of the tumour via anterior orbitotomy and eyelid reconstruction were performed. Histopathology report reviewed plexiform neurofibroma of the lacrimal gland. Further physical examination confirmed presence of multiple café-au-lait spots. He was diagnosed as Neurofibromatosis Type 1.
format	Article
author	Poh, Khay Wei Syed Osman SIH,
spellingShingle	Poh, Khay Wei Syed Osman SIH, A rare presentation of plexiform neurofibroma
author_facet	Poh, Khay Wei Syed Osman SIH,
author_sort	Poh, Khay Wei
title	A rare presentation of plexiform neurofibroma
title_short	A rare presentation of plexiform neurofibroma
title_full	A rare presentation of plexiform neurofibroma
title_fullStr	A rare presentation of plexiform neurofibroma
title_full_unstemmed	A rare presentation of plexiform neurofibroma
title_sort	rare presentation of plexiform neurofibroma
publisher	Pusat Perubatan Universiti Kebangsaan Malaysia
publishDate	2018
url	http://journalarticle.ukm.my/12556/ http://journalarticle.ukm.my/12556/ http://journalarticle.ukm.my/12556/1/8._poh__syed.pdf
first_indexed	2023-09-18T20:02:52Z
last_indexed	2023-09-18T20:02:52Z
_version_	1777406965605990400

A rare presentation of plexiform neurofibroma

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