Primary pigmented nodular adrenocortical disease

Primary pigmented nodular adrenocortical disease

Primary pigmented nodular adrenocortical disease (PPNAD) is a rare adrenal tumour causing corticotrophin-independent Cushing's syndrome. It occurs mainly in children and young adults. The histological examination is characterised by small pigmented micronodules on the adrenal cortex. The diagno...

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Main Authors: Ngow, Harris Abdullah, Khairina, Wan Mohd Nowalid Wan
Format: Article
Language:English
Published: The Polish Society of Endocrinology 2011
Subjects:
RB Pathology
RC Internal medicine
Online Access:http://irep.iium.edu.my/5111/
http://irep.iium.edu.my/5111/
http://irep.iium.edu.my/5111/1/EP.2011.3_17_Ngow.pdf
id iium-5111
recordtype eprints
spelling iium-51112011-10-28T05:20:02Z http://irep.iium.edu.my/5111/ Primary pigmented nodular adrenocortical disease Ngow, Harris Abdullah Khairina, Wan Mohd Nowalid Wan RB Pathology RC Internal medicine Primary pigmented nodular adrenocortical disease (PPNAD) is a rare adrenal tumour causing corticotrophin-independent Cushing's syndrome. It occurs mainly in children and young adults. The histological examination is characterised by small pigmented micronodules on the adrenal cortex. The diagnosis is most often seen in patients with Carney Complex, but it can also occur in isolation. We report a case of Carney Complex that was referred for adrenalectomy. The procedure was uneventful and the patient was well at discharge. The adrenal pathology showed numerous black nodules measuring less than 2mm in diameter. This feature was pathognomonic of primary pigmented nodular adrenocortical disease. The Polish Society of Endocrinology 2011 Article PeerReviewed application/pdf en http://irep.iium.edu.my/5111/1/EP.2011.3_17_Ngow.pdf Ngow, Harris Abdullah and Khairina, Wan Mohd Nowalid Wan (2011) Primary pigmented nodular adrenocortical disease. Endokrynologia Polska/ Polish Journal of Endocrinology, 62 (3). pp. 268-70. ISSN 0423-104X http://www.endokrynologia.polska.viamedica.pl
repository_type Digital Repository
institution_category Local University
institution International Islamic University Malaysia
building IIUM Repository
collection Online Access
language English
topic RB Pathology
RC Internal medicine
spellingShingle RB Pathology
RC Internal medicine
Ngow, Harris Abdullah
Khairina, Wan Mohd Nowalid Wan
Primary pigmented nodular adrenocortical disease
description Primary pigmented nodular adrenocortical disease (PPNAD) is a rare adrenal tumour causing corticotrophin-independent Cushing's syndrome. It occurs mainly in children and young adults. The histological examination is characterised by small pigmented micronodules on the adrenal cortex. The diagnosis is most often seen in patients with Carney Complex, but it can also occur in isolation. We report a case of Carney Complex that was referred for adrenalectomy. The procedure was uneventful and the patient was well at discharge. The adrenal pathology showed numerous black nodules measuring less than 2mm in diameter. This feature was pathognomonic of primary pigmented nodular adrenocortical disease.
format Article
author Ngow, Harris Abdullah
Khairina, Wan Mohd Nowalid Wan
author_facet Ngow, Harris Abdullah
Khairina, Wan Mohd Nowalid Wan
author_sort Ngow, Harris Abdullah
title Primary pigmented nodular adrenocortical disease
title_short Primary pigmented nodular adrenocortical disease
title_full Primary pigmented nodular adrenocortical disease
title_fullStr Primary pigmented nodular adrenocortical disease
title_full_unstemmed Primary pigmented nodular adrenocortical disease
title_sort primary pigmented nodular adrenocortical disease
publisher The Polish Society of Endocrinology
publishDate 2011
url http://irep.iium.edu.my/5111/
http://irep.iium.edu.my/5111/
http://irep.iium.edu.my/5111/1/EP.2011.3_17_Ngow.pdf
first_indexed 2023-09-18T20:13:36Z
last_indexed 2023-09-18T20:13:36Z
_version_ 1777407639968284672

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