Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?

A 39-year-old man was diagnosed with von Hippel-Lindau syndrome, which was associated with retinal haemangioblastoma, cervical cord haemangioblastoma and bilateral renal cell carcinoma. He subsequently underwent an arterial embolisation and cervical laminectomy, following a spinal angiogram o...

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Main Authors: Mohd Shah, Azarisman Shah, K, Nor Azmi
Format: Article
Language:English
Published: Singapore Medical Association 2007
Subjects:
Online Access:http://irep.iium.edu.my/17108/
http://irep.iium.edu.my/17108/
http://irep.iium.edu.my/17108/1/Renal_cell_carcinoma_in_a_von_Hippel-.pdf
id iium-17108
recordtype eprints
spelling iium-171082012-01-26T09:31:10Z http://irep.iium.edu.my/17108/ Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? Mohd Shah, Azarisman Shah K, Nor Azmi RC0254 Neoplasms. Tumors. Oncology (including Cancer) A 39-year-old man was diagnosed with von Hippel-Lindau syndrome, which was associated with retinal haemangioblastoma, cervical cord haemangioblastoma and bilateral renal cell carcinoma. He subsequently underwent an arterial embolisation and cervical laminectomy, following a spinal angiogram of the cervical lesion. He also had a right radical nephrectomy, with no perioperative complications. However, on admission for the left radical nephrectomy, he was noted to have preoperative hypertension. Further investigation revealed an enlarged left adrenal gland on abdominal computed tomography scan and raised urinary catecholamines. We discuss the risk of renal cell carcinoma a nd ph a e oc h romoc y toma a r i s ing concomitantly in von Hippel-Lindau syndrome, and how best to investigate and manage them. Singapore Medical Association 2007 Article PeerReviewed application/pdf en http://irep.iium.edu.my/17108/1/Renal_cell_carcinoma_in_a_von_Hippel-.pdf Mohd Shah, Azarisman Shah and K, Nor Azmi (2007) Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated? Singapore Medical Journal, 48(8) (779). ISSN 0037-5675 http://smj.sma.org.sg/smjcurrent.html
repository_type Digital Repository
institution_category Local University
institution International Islamic University Malaysia
building IIUM Repository
collection Online Access
language English
topic RC0254 Neoplasms. Tumors. Oncology (including Cancer)
spellingShingle RC0254 Neoplasms. Tumors. Oncology (including Cancer)
Mohd Shah, Azarisman Shah
K, Nor Azmi
Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?
description A 39-year-old man was diagnosed with von Hippel-Lindau syndrome, which was associated with retinal haemangioblastoma, cervical cord haemangioblastoma and bilateral renal cell carcinoma. He subsequently underwent an arterial embolisation and cervical laminectomy, following a spinal angiogram of the cervical lesion. He also had a right radical nephrectomy, with no perioperative complications. However, on admission for the left radical nephrectomy, he was noted to have preoperative hypertension. Further investigation revealed an enlarged left adrenal gland on abdominal computed tomography scan and raised urinary catecholamines. We discuss the risk of renal cell carcinoma a nd ph a e oc h romoc y toma a r i s ing concomitantly in von Hippel-Lindau syndrome, and how best to investigate and manage them.
format Article
author Mohd Shah, Azarisman Shah
K, Nor Azmi
author_facet Mohd Shah, Azarisman Shah
K, Nor Azmi
author_sort Mohd Shah, Azarisman Shah
title Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?
title_short Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?
title_full Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?
title_fullStr Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?
title_full_unstemmed Renal cell carcinoma in a von Hippel-Lindau syndrome; when should pheochromocytoma be anticipated?
title_sort renal cell carcinoma in a von hippel-lindau syndrome; when should pheochromocytoma be anticipated?
publisher Singapore Medical Association
publishDate 2007
url http://irep.iium.edu.my/17108/
http://irep.iium.edu.my/17108/
http://irep.iium.edu.my/17108/1/Renal_cell_carcinoma_in_a_von_Hippel-.pdf
first_indexed 2023-09-18T20:25:55Z
last_indexed 2023-09-18T20:25:55Z
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